Non-positional Leg Defects: Difference between revisions
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'''Pes equinovarus congenitus''' (''PEC'',''talipes equinovarus'', | '''Pes''' '''equinovarus''' '''congenitus''' ( ''PEC'' , ''talipes equinovarus'' , English ''clubfoot'' , German ''Klumpfuss'' ) is the most common non-positional [[Vrozené vady končetin|congenital defect of the leg]] (1:1000) and the 2nd most common developmental defect in orthopedics (after [[Vývojová dysplázie kyčelní|DDH]] ). | ||
It can be a postural (fully conservatively correctable) or structural defect. | |||
Famous personalities with this defect included, for example, the Roman Emperor Claudius, the poet George Gordon Byron or the Nazi propaganda minister Joseph Goebbels. | |||
* | * boys are more often affected (2:1), in ½ cases the defect is bilateral | ||
* | * in 10% associated with other congenital defects ( [[Vývojová dysplázie kyčelní|DDH]] , [[Hernia|hernias]] , [[Meningokéla|meningomyelocele]] ) | ||
* | * the main factor in the creation and maintenance of this deformity is the pull of the tibialis posterior muscle, longer medial subluxation in the [[Chopartův kloub|Chopart joint]] and shortening of the Achilles tendon | ||
== | ==Characteristics== | ||
[[Soubor:PEC.jpg|náhled|Klinický obraz PEC.]] | [[Soubor:PEC.jpg|náhled|Klinický obraz PEC.]] | ||
* | * equinox position in the [[Hlezenní kloub|ankle joint]] (fall of the tip of the foot plantarly) | ||
* | * heel varus (the heel is turned inwards when viewed from the back – heel bone supination) | ||
* | * excavation (arching of the middle part of the foot) | ||
* | * inversion of the forefoot (caused by a combination of adduction and supination of the forefoot) – i.e. the front part of the foot deviates from the longitudinal axis of the foot in the direction of the thumb and is placed on the outer edge | ||
* | * medial subluxation in the talonavicular joint | ||
* | * internal torsion of the [[tibia]] (can only be a consequence) | ||
== | ==Etiology== | ||
It is multifactorial, the etiology is not exactly known, there are several theories: | |||
#''' | # '''theory of neuromuscular defect''' – striated muscle defect / intrauterine lesion of the peroneus nerve | ||
#''' | # '''mechanical theory''' – arrest of talus development during arrest of leg rotation during intrauterine development | ||
#''' | # '''theory of primary bone dysplasia''' – congenitally defective shape of the talus | ||
Structural PEC also occurs in connection with [[Edwardsův syndrom|Edwards syndrome]] , [[Oligohydramnion|oligohydramnios]] , [[Vrozené vady končetin|congenital constriction band syndrome]] or [[Meningokéla|spina bifida cystica]] | |||
== | ==Pathogenesis== | ||
* | * due to the predominance of the muscles on the medial side of the foot (main pull of the tibialis posterior muscle), the leg twists into a cone-shaped deformation, the foot steps on the outer edge, calluses or ulcerations form in places of non-physiological stress, as well as early arthrosis of the leg joints | ||
* | * susceptibility to relapse | ||
== | ==Pathological-anatomical findings== | ||
* | * [[Ossa tarsi#Talus|'''talus''']] – head with neck curled plantarly and medially, sinus tarsi laterally, | ||
* | * [[Ossa tarsi#Os%20naviculare|'''navicular axis''']] – medially dislocated, | ||
* | * [[Ossa tarsi#Calcaneus|'''calcaneus''']] – front part curled medially, | ||
*''' | * [[Fibula|'''fibula''']] – displaced dorsally, | ||
*''' | * '''Achilles tendon''' - shortened. | ||
== | ==Clinical picture== | ||
* | * foot in plantar flexion | ||
* | * heel smaller, varus and pulled up towards the outer ankle, the outer ankle is further back and protrudes | ||
* | * on the medial side in the area of the heel a deep skin groove | ||
* | * forefoot in adduction and supination, varus and equinus | ||
* | * Achilles tendon shortened and strained | ||
* | * calf hypotrophy, shorter flat leg | ||
* | * in most cases there is no difference in limb lengths | ||
== | ==Classification (Lehman and Tachdjian)== | ||
#''' | # '''position type PEC''' | ||
#''' | # '''right – rigid PEC type''' | ||
#''' | # '''resistant rigid type''' , associated with other congenital defects or [[Artrogrypóza|arthrogryposis]] | ||
* | * positional PEC is quickly corrected after exercise, but untreated it can turn into a rigid form | ||
* | * rigid PEC always indicated for operative solution | ||
== | ==X-ray examination== | ||
In the lateral and dorsoplantar projection, we evaluate 3 angles: | |||
*''''' | * '''''Kite's angle''''' (dorsoplantar TC angle) – the angle between the longitudinal axis of the calcaneus and talus, norm: > 20°, PEC: calcaneus and talus axes almost parallel | ||
*''''' | * '''''angle between the axis of the talus and the longitudinal axis of the 1st metatarsal''''' – norm: < 20°, PEC: > 20° | ||
*''''' | * '''''talocalcaneal''' '''angle''''' (lateral TC angle) – evaluated in lateral projection, norm: > 35°, increases in dorsiflexion (with eversion of the calcaneus), decreases in plantiflexion (with inversion of the calcaneus), PEC: 15°, decreases in dorsiflexion, in the plantar increases | ||
*''' | * '''talocalcaneal''' '''index''' – sum of TC angles in both projections, value less than 40° – incomplete healing | ||
==Therapy== | |||
* with the aim of creating a shapely and functionally normal leg | |||
* inform parents that the leg will almost always remain shorter and the calf weaker, that healing lasts from birth to adolescence | |||
* treatment must be carried out carefully to avoid bone damage (risk of osteonecrosis) | |||
== Conservative therapy == | |||
It goes hand in hand with surgical treatment, simple conservative treatment is sufficient for positional PEC therapy. The essence is the release of muscle and ligament contractures and the achievement of dislocation reposition in the talonaviculocuneiform joint (however, this is impossible with the right PEC). | |||
* immediately after detecting the defect: '''corrective''' exercises, untying, corrective plaster bandages (for small children and rigid forms we change them every week, for older children we leave them for 14 days / we make sensing splints made of plastic, they reach from the toes to the groin in 70-90° flexion of the knee joint , we correct all 3 components of the deformity) | |||
* '''after the correction part of the treatment, the retention''' treatment begins (retention plaster bandages, laminate splints, ''Denisov-Brown splints'' - shoes without a toe with a connecting rod) | |||
* '''Kite's conservative therapy''' - corrected each component separately and sequentially (forefoot adduction → heel varus → foot equinus) | |||
* '''Ponseti's conservative therapy''' (1996) - correction of all components of the deformity at the same time (correction of forefoot adduction, lateral subtalar derotation and inversion correction), achieving correction with less than 10 changes of straightening plaster casts, to overcome equinosity adds subcutaneous Achilles tendon tenotomy, after putting aside Denisov plaster cast -Brown splint up to 6 years of age | |||
===Surgical therapy=== | |||
* it usually starts around 6-8. months of the child's age | |||
* the so-called path of small steps / one-time complete correction | |||
* only the first operation has any hope of success | |||
=== Surgery on soft parts (tendons, joint capsules, ligaments) === | |||
* '''We lengthen the tendons''' in different ways (Achilles tendon (Z-cut), tibialis post tendon, flexor hallucis lg., flexor digitorum lg.) or transpose (e.g. tibialis ante tendon [[Musculus tibialis anterior|from]] attachment to 1. metatarsus on the outside of the dorsum of the foot) | |||
* we cross '''joint capsules''' (medial and dorsal capsulotomy, e.g. talonavicular joint, naviculocuneiform joint, talocrural joint), plantar aponeurosis or ligaments connecting the individual bones of the tarsus | |||
====Skeleton surgery==== | |||
We operate on the skeleton later (at least after the 3rd year, but more likely after the 6th year of age). | |||
==== | * '''calcaneal''' '''osteotomy''' (to correct varus) | ||
* '''forefoot''' '''osteotomy''' (to correct forefoot adduction) | |||
* '''arthrodesis''' (e.g. triple subtalar arthrodesis as a definitive solution to residual PEC deformities after treatment) – at least after 12, preferably after 15 years of age | |||
====Complete performances==== | |||
* '''operation according to Turco''' – posteromedial release of all mentioned joints, lengthening of the Achilles tendon, tendons of the flexors of the fingers and big toe, release / lengthening of the tendon of the tibialis post. feet over the calcaneus, and with the other we fix the navicular bone with the talus and metatarsals, we fix the whole thing with a plaster bandage min. 12 weeks, after 6 weeks we replaster, remove sutures and transfixation, in the 4th month we allow full weight bearing in modeled shoes | |||
* '''operation according to McKay''' - more radical and complex, suitable for up to 3 years, it is a plantar (complete subtalar) release - from a wide circular surgical approach, after dissection of the suralis nerve and the nerve-vascular bundle behind the inner ankle, we completely release the talus and calcaneus so that they could rotate the talus against the calcaneus and secure it in the correct position with K-wires, the next procedure is the same (plastering and corrective shoes) | |||
<noinclude> | <noinclude> | ||
==Odkazy== | ==Odkazy== | ||
===Související články=== | ===Související články=== | ||
Revision as of 11:00, 11 February 2023
Non-positional defects of the leg (the leg cannot be corrected into the correct position) are very serious, their treatment is complex and long, often surgical.
Pes equinovarus congenitus
Pes equinovarus congenitus ( PEC , talipes equinovarus , English clubfoot , German Klumpfuss ) is the most common non-positional congenital defect of the leg (1:1000) and the 2nd most common developmental defect in orthopedics (after DDH ).
It can be a postural (fully conservatively correctable) or structural defect.
Famous personalities with this defect included, for example, the Roman Emperor Claudius, the poet George Gordon Byron or the Nazi propaganda minister Joseph Goebbels.
- boys are more often affected (2:1), in ½ cases the defect is bilateral
- in 10% associated with other congenital defects ( DDH , hernias , meningomyelocele )
- the main factor in the creation and maintenance of this deformity is the pull of the tibialis posterior muscle, longer medial subluxation in the Chopart joint and shortening of the Achilles tendon
Characteristics
- equinox position in the ankle joint (fall of the tip of the foot plantarly)
- heel varus (the heel is turned inwards when viewed from the back – heel bone supination)
- excavation (arching of the middle part of the foot)
- inversion of the forefoot (caused by a combination of adduction and supination of the forefoot) – i.e. the front part of the foot deviates from the longitudinal axis of the foot in the direction of the thumb and is placed on the outer edge
- medial subluxation in the talonavicular joint
- internal torsion of the tibia (can only be a consequence)
Etiology
It is multifactorial, the etiology is not exactly known, there are several theories:
- theory of neuromuscular defect – striated muscle defect / intrauterine lesion of the peroneus nerve
- mechanical theory – arrest of talus development during arrest of leg rotation during intrauterine development
- theory of primary bone dysplasia – congenitally defective shape of the talus
Structural PEC also occurs in connection with Edwards syndrome , oligohydramnios , congenital constriction band syndrome or spina bifida cystica
Pathogenesis
- due to the predominance of the muscles on the medial side of the foot (main pull of the tibialis posterior muscle), the leg twists into a cone-shaped deformation, the foot steps on the outer edge, calluses or ulcerations form in places of non-physiological stress, as well as early arthrosis of the leg joints
- susceptibility to relapse
Pathological-anatomical findings
- talus – head with neck curled plantarly and medially, sinus tarsi laterally,
- navicular axis – medially dislocated,
- calcaneus – front part curled medially,
- fibula – displaced dorsally,
- Achilles tendon - shortened.
Clinical picture
- foot in plantar flexion
- heel smaller, varus and pulled up towards the outer ankle, the outer ankle is further back and protrudes
- on the medial side in the area of the heel a deep skin groove
- forefoot in adduction and supination, varus and equinus
- Achilles tendon shortened and strained
- calf hypotrophy, shorter flat leg
- in most cases there is no difference in limb lengths
Classification (Lehman and Tachdjian)
- position type PEC
- right – rigid PEC type
- resistant rigid type , associated with other congenital defects or arthrogryposis
- positional PEC is quickly corrected after exercise, but untreated it can turn into a rigid form
- rigid PEC always indicated for operative solution
X-ray examination
In the lateral and dorsoplantar projection, we evaluate 3 angles:
- Kite's angle (dorsoplantar TC angle) – the angle between the longitudinal axis of the calcaneus and talus, norm: > 20°, PEC: calcaneus and talus axes almost parallel
- angle between the axis of the talus and the longitudinal axis of the 1st metatarsal – norm: < 20°, PEC: > 20°
- talocalcaneal angle (lateral TC angle) – evaluated in lateral projection, norm: > 35°, increases in dorsiflexion (with eversion of the calcaneus), decreases in plantiflexion (with inversion of the calcaneus), PEC: 15°, decreases in dorsiflexion, in the plantar increases
- talocalcaneal index – sum of TC angles in both projections, value less than 40° – incomplete healing
Therapy
- with the aim of creating a shapely and functionally normal leg
- inform parents that the leg will almost always remain shorter and the calf weaker, that healing lasts from birth to adolescence
- treatment must be carried out carefully to avoid bone damage (risk of osteonecrosis)
Conservative therapy
It goes hand in hand with surgical treatment, simple conservative treatment is sufficient for positional PEC therapy. The essence is the release of muscle and ligament contractures and the achievement of dislocation reposition in the talonaviculocuneiform joint (however, this is impossible with the right PEC).
- immediately after detecting the defect: corrective exercises, untying, corrective plaster bandages (for small children and rigid forms we change them every week, for older children we leave them for 14 days / we make sensing splints made of plastic, they reach from the toes to the groin in 70-90° flexion of the knee joint , we correct all 3 components of the deformity)
- after the correction part of the treatment, the retention treatment begins (retention plaster bandages, laminate splints, Denisov-Brown splints - shoes without a toe with a connecting rod)
- Kite's conservative therapy - corrected each component separately and sequentially (forefoot adduction → heel varus → foot equinus)
- Ponseti's conservative therapy (1996) - correction of all components of the deformity at the same time (correction of forefoot adduction, lateral subtalar derotation and inversion correction), achieving correction with less than 10 changes of straightening plaster casts, to overcome equinosity adds subcutaneous Achilles tendon tenotomy, after putting aside Denisov plaster cast -Brown splint up to 6 years of age
Surgical therapy
- it usually starts around 6-8. months of the child's age
- the so-called path of small steps / one-time complete correction
- only the first operation has any hope of success
Surgery on soft parts (tendons, joint capsules, ligaments)
- We lengthen the tendons in different ways (Achilles tendon (Z-cut), tibialis post tendon, flexor hallucis lg., flexor digitorum lg.) or transpose (e.g. tibialis ante tendon from attachment to 1. metatarsus on the outside of the dorsum of the foot)
- we cross joint capsules (medial and dorsal capsulotomy, e.g. talonavicular joint, naviculocuneiform joint, talocrural joint), plantar aponeurosis or ligaments connecting the individual bones of the tarsus
Skeleton surgery
We operate on the skeleton later (at least after the 3rd year, but more likely after the 6th year of age).
- calcaneal osteotomy (to correct varus)
- forefoot osteotomy (to correct forefoot adduction)
- arthrodesis (e.g. triple subtalar arthrodesis as a definitive solution to residual PEC deformities after treatment) – at least after 12, preferably after 15 years of age
Complete performances
- operation according to Turco – posteromedial release of all mentioned joints, lengthening of the Achilles tendon, tendons of the flexors of the fingers and big toe, release / lengthening of the tendon of the tibialis post. feet over the calcaneus, and with the other we fix the navicular bone with the talus and metatarsals, we fix the whole thing with a plaster bandage min. 12 weeks, after 6 weeks we replaster, remove sutures and transfixation, in the 4th month we allow full weight bearing in modeled shoes
- operation according to McKay - more radical and complex, suitable for up to 3 years, it is a plantar (complete subtalar) release - from a wide circular surgical approach, after dissection of the suralis nerve and the nerve-vascular bundle behind the inner ankle, we completely release the talus and calcaneus so that they could rotate the talus against the calcaneus and secure it in the correct position with K-wires, the next procedure is the same (plastering and corrective shoes)
Odkazy
Související články
- Vrozené vady končetin
- Vývojová dysplázie kyčelní
- Arthrogryposis multiplex congenita
- Diastrofický dwarfismus
- Vývojová dysplázie kyčelní
- Vrozené vývojové vady
Použitá literatura
Externí odkazy
- Achilleus, z.s. pacientská organizace, sdružuje rodiče a dospělé s vrozenou vadou
- Ponseti metoda. odborné stránky věnující se podrobně VVV pes equinovarus, provozuje Achilleus z.s.
- MedlinePlus Medical Encyclopedia
- eMedicine, Orthopedic Surgery
- Clubfoot.co.uk
Kategorie:Ortopedie Kategorie:Genetika Kategorie:Pediatrie
Metatarsus varus
__
Metatarsus varus (pes adductus, metatarsus adductus) is a non-positional foot defect. Congenitally varus metatarsals can be of three types:
Metatarsus varus congenitus
This is a medial subluxation in the tarsometatarsal joints (Lisfranc joint).
- Clinical picture
- all metatarsals in adduction (forefoot curled inward) and inversion
- heel in neutral position / slight valgus
- child walks with toes inward, medial edge of foot concave, outer edge convex
- Therapy
- requires intensive treatment
- always conservative at first: start with exercise (pressure on medial surface to align foot to correct position), a series of corrective plaster bandages over the knee, modeled so that corrective pressure is directed over metatarsals laterally (duration of individual fixations 1-2 weeks, 6-8 weeks overall, rarely longer)
- if the deformity persists: around the age of 2 years operations on soft tissues (tendons and joint capsules), from the age of 3 years osteotomy over the metatarsal bases followed by transfixation with Kirschner wires and plaster fixation for 6 weeks (however, it is better to wait until the child is 5-6 years old, when there is no longer a risk of injury to the growth splays)
Sickle foot
- synonyms: dog serpens, skewfoot, zig-zag fuss
- rare defect
- Clinical picture
- metatarsal varicosity, heel valgus
- talocrural joint in anteroposterior projection on rtg spherical
- toe retracted into adduction most, forefoot creates a bayonet-like deformity (pes serpens)
- Therapy
- treatment is initiated conservatively (RHB and cast fixation)
- if unsuccessful, operate (capsulotomy, tendon intersection of m. abductor hallucis, osteotomy of the calcaneus)
Residual deformity
- after treatment PEC
- cases where adduction of the forefoot persists
References
References used
- DUNGL, P.. Ortopedie. 1. edition. Grada Publishing, 2005. ISBN 80-247-0550-8.
- SOSNA, A. – VAVŘÍK, P. – KRBEC, M.. Základy ortopedie. 1. edition. Triton, 2001. ISBN 80-7254-202-8.
- KOUDELA, K.. Ortopedie. 1. edition. Karolinum, 2004. ISBN 80-246-0654-2.
Related articles
- Congenital defects of the limbs
- Arthrogryposis multiplex congenita
- Non-union of leg defects
- Positional foot defects
- Pes equinovarus congenitus
Vrozený strmý talus
Digitus V. supraductus
Přeložený malíček je často familiárního výskytu.
Klinické projevy
- malíček uchýlen mediálně tak, že se překládá přes ostatní prsty
- většinou činí obtíže v obuvi
Terapie
- zpočátku se snažíme udržovat prst ve správném postavení pomocí proužků náplasti
- při nezdaru indikována operace spočívající v kožních, ev. šlachových plastikách
Ostatní (a vzácnější) vrozené vady nohy
- deformity nohy při arthrogryposis multiplex congenita (pes equinovarus, talus verticalis)
- koalice tarzálních kostí (nejčastěji talokalkaneární a kalkaneonavikulární)
- vrozeně varózní postavení prstů (1 nebo více malých prstů stočeno mediálně a plantárně, v distálním interfalangeálním kloubu terminální článek stočen do supinace)
- vrozený hallux varus (u tříčlánkového palce, kde střední článek vytvořen jen rudimentárně ve formě klínu, palec v metatarzofalangeálním kloubu uchýlen mediálně)
- vrozené makrodaktylie (nahromaděním vazivově-tukové tkáně či při neurofibromatóze), mikrodaktylie (izolovaně či v kombinaci s hypoplasií příslušného metatarzu – brachymetafonie, obvyklý nález u Streeterovy dysplázie), syndaktylie či polydaktylie (preaxiální, postaxiální či centrální) – viz Vrozené vady končetin
- vrozené kladívkovité prsty (digiti malei, prsty v základním metatarzofalangeálním kloubu v dorzální flexi, v prvním interfalangeálním kloubu ve flexi, u starších dětí bolestivé kalozity)
- vrozené zkrácení metatarzů (časté v Japonsku)
- vrozený rozštěp nohy (parciální adaktylie, má tvar klepeta – lobster claw)
- nadpočetné kůstky nohy
Odkazy
Související články
- Polohové vady nohy
- Vrozené vady končetin
- Arthrogryposis multiplex congenita
- Pes equinovarus congenitus
- Pes planovalgus
- Diastrofický dwarfismus
- Vývojová dysplázie kyčelní
- Vrozené vývojové vady
