Eisenmenger's syndrome

eisenmengers syndrome

Schematic picture describing the principle of Eisenmenger syndrome
Clinical picture	stiffness-clubbed fingers-cyanosis
Diagnostika	ECG- chest xray- ECHO
Therapy	cannot be cured

Eisenmenger's syndrome is a short-circuit defect at any level (aortopulmonary, atrial, ventricular) along with secondary pulmonary hypertension. It results in the change of the original left-right short circuit to right-left.

• Pulmonary hypertension significant;
• pathogenesis unclear (pulmonary burden on the volume of recirculating blood);
• media hypertrophy, fibrotization and cellular infiltration of the intima of the pulmonary branches (pulmonary vascular disease);
• hypertrophy and right ventricular insufficiency (insufficiency of the tricuspid valve).

Clinical picture

• Progressive dyspnea;
• clubbed fingers;
• cyanosis.

Diagnostics

• Tricuspid insufficiency (prominent wave "a" on the venous pulse in the neck);
• curious right ventricular stroke subxifoidally;
• systolic ejection crank; systolic murmur above the lungs with emphasis II. echoes;
• ECG: hypertrophy of the right atrium with prominence of P wave in leads II, III, aVF;
• Chest x-ray: prominence of the pulmonary arch;
• ECHO: presence of congenital heart disease, signs of pulmonary hypertension, consequences.

Therapy

• Eisenmenger syndrome cannot be treated;
• important prevention by cardiac surgery in childhood;
• heart and lung transplantation;
• reason for abortion for health reasons.

Links

related articles

• congenital heart defects
• Congenital malformations

References

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