Chiari malformation: Difference between revisions
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(Original text from WikiSkripta: Chiariho malformace https://www.wikiskripta.eu/w/Chiariho_malformace) |
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[[File:MRI of human brain with type-1 Arnold-Chiari malformation and herniated cerebellum.jpg|thumb|Brain MRI showing herniation of cerebellar tonsils into the foramen magnum in a patient with '''Arnold-Chiari malformation''' of the first type]] | [[File:MRI of human brain with type-1 Arnold-Chiari malformation and herniated cerebellum.jpg|thumb|Brain MRI showing herniation of cerebellar tonsils into the foramen magnum in a patient with '''Arnold-Chiari malformation''' of the first type]] | ||
'''Chiari malformation''' (''Arnold-Chiari malformation'') is a '''congenital CNS anomaly'''. It is a '''dystopia''' of the [[mozeček|cerebellum]] ''' and ''' [[medulla oblongata]] into the '''spinal canal''', which is clinically manifested by [[hydrocefalus|hydrocephalus]]. RWe distinguish four types of rhombencephalon abnormalities (cerebellum, pons, oblongata): | '''Chiari malformation''' (''Arnold-Chiari malformation'') is a '''congenital CNS anomaly'''. It is a '''dystopia''' of the [[mozeček|cerebellum]] ''' and ''' [[medulla oblongata]] into the '''spinal canal''', which is clinically manifested by [[hydrocefalus|hydrocephalus]]. RWe distinguish four types of rhombencephalon abnormalities (cerebellum, pons, oblongata): | ||
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* {{Citace|typ = web|příjmení1 = Beneš|jméno1 = Jiří|název = Studijní materiály|rok = 2007|citováno = 2010|url = http://jirben.wz.cz}} | * {{Citace|typ = web|příjmení1 = Beneš|jméno1 = Jiří|název = Studijní materiály|rok = 2007|citováno = 2010|url = http://jirben.wz.cz}} | ||
=== References === | === References === | ||
*[[ws:Chiariho malformace]] | |||
* {{Citace | * {{Citace | ||
|typ = kniha | |typ = kniha | ||
Latest revision as of 19:45, 18 May 2022
Chiari malformation (Arnold-Chiari malformation) is a congenital CNS anomaly. It is a dystopia of the cerebellum and medulla oblongata into the spinal canal, which is clinically manifested by hydrocephalus. RWe distinguish four types of rhombencephalon abnormalities (cerebellum, pons, oblongata):
- Type 1 - herniation of the cerebellar tonsil under the foramen magnum, IV. the chamber is stored normally
- Type 2 - usually the co-presence of myelomeningocele
- Type 3 - severe dislocation of structures in the posterior pit, often associated with suboccipital encephalomeningocele; usually incompatible with life
- Type 4 - cerebellar hypoplasia without herniation.
Clinical picture[edit | edit source]
Clinically, the defect is manifested mainly by headache, weakened grip and spasticity of DK.
Diagnosis[edit | edit source]
Native X-ray, MRI.
Therapy[edit | edit source]
The main problem is hydrocephalus – decompression of the craniospinal junction, short-circuit drainage operations.
