Binder syndrome

From WikiLectures

Synonyms: dysosteosis maxillonasalis, dysplasia maxillonasalis.

Named after the Austrian dentist Kurt Binder.

Genetics
  • OMIM: 155050
  • The etiology is probably heterogeneous, if the syndrome repeats in families, then it shows autosomal dominant inheritance.[1]
Characteristics
  • flat short nose,
  • crescent shaped nostrils,
  • the base of the upper jaw is flat,
  • pseudoprogeny,
  • hypoplasia to aplasia of the sinus frontalis and the anterior nasal process of the jaw.


Links[edit | edit source]

Reference[edit | edit source]

  1. OMIM : Binders syndrome - Clinical synopsis [database]. Johns Hopkins University. [cit. 2011-04-24]. <http://omim.org/entry/155050>.

References[edit | edit source]

  • LAZOVSKIS, Ilmars – DOBIÁŠ, Václav. Overview of clinical symptoms and syndromes. 2. edition. Avicenum, zdravotnické nakladatelství, 1990. 0 pp. ISBN 80-201-0043-1.